ARG58844
anti-Galactosidase alpha antibody
anti-Galactosidase alpha antibody for ICC/IF,Western blot and Human,Mouse
概述
产品描述 | Rabbit Polyclonal antibody recognizes Galactosidase alpha |
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反应物种 | Hu, Ms |
应用 | ICC/IF, WB |
宿主 | Rabbit |
克隆 | Polyclonal |
同位型 | IgG |
靶点名称 | Galactosidase alpha |
抗原物种 | Human |
抗原 | Recombinant fusion protein corresponding to aa. 150-429 of Human Galactosidase alpha (NP_000160.1). |
偶联标记 | Un-conjugated |
別名 | Alpha-galactosidase A; Melibiase; Alpha-D-galactosidase A; Alpha-D-galactoside galactohydrolase; EC 3.2.1.22; Agalsidase; GALA |
应用说明
应用建议 |
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应用说明 | * The dilutions indicate recommended starting dilutions and the optimal dilutions or concentrations should be determined by the scientist. | ||||||
实际分子量 | 49 kDa |
属性
形式 | Liquid |
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纯化 | Affinity purified. |
缓冲液 | PBS (pH 7.3), 0.02% Sodium azide and 50% Glycerol. |
抗菌剂 | 0.02% Sodium azide |
稳定剂 | 50% Glycerol |
存放说明 | For continuous use, store undiluted antibody at 2-8°C for up to a week. For long-term storage, aliquot and store at -20°C. Storage in frost free freezers is not recommended. Avoid repeated freeze/thaw cycles. Suggest spin the vial prior to opening. The antibody solution should be gently mixed before use. |
注意事项 | For laboratory research only, not for drug, diagnostic or other use. |
生物信息
数据库连接 | |
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基因名称 | GLA |
全名 | galactosidase, alpha |
背景介绍 | This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq, Jul 2008] |
细胞定位 | Lysosome. [UniProt] |
预测分子量 | 49 kDa |
检测图片 (1) Click the Picture to Zoom In